alpha L Idosiduronase

《英文msh词典》alpha L Idosiduronase
[入口词] alpha L Idosiduronase
[主题词] Iduronidase
[英文释义] An enzyme that hydrolyzes iduronosidic linkages in desulfated dermatan. Deficiency of this enzyme produces Hurler's syndrome. EC 3.2.1.76.